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Case Report

Open Access

Pulmonary hypertension leading to right heart failure in a patient with iga gammopathy


1nternal Medicine, St Elizabeth’s Hospital, Belmont Avenue, Youngstown

DOI: 10.22514/SV21.042007.7 Vol.2,Issue 1,April 2007 pp.29-32

Published: 20 April 2007

*Corresponding Author(s): YASHVIR S. SANGWAN E-mail:

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Amyloidosis is a rare disorder characterized by the deposition of amorphous, extracellular, insoluble fibrillar protein in various tissues of the body. Pulmonary hypertension usually occurs in the last stages of the disease with co-existing left ventricular failure. Amyloidosis causing pulmonary hypertension in a patient with no evidence of left ventricular failure is rarely mentioned in literature. Here, we present a patient with IgA gammopathy presenting with pulmonary hypertension leading to progressive right heart failure and death.

Key words

amyloidosis, pulmonary hypertension, IgA gammopathy

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YASHVIR S. SANGWAN,BHAGWAN DASS. Pulmonary hypertension leading to right heart failure in a patient with iga gammopathy. Signa Vitae. 2007. 2(1);29-32.


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